CASE REPORT   

Journal of Neurosurgical Sciences 2020 June;64(3):287-90

DOI: 10.23736/S0390-5616.16.03612-2

Copyright © 2016 EDIZIONI MINERVA MEDICA

lingua: Inglese

Multiple cerebral arteriovenous malformations associated to rostral hypoplasia of the superior sagittal sinus: a case report

Ramon TORNÉ ✉, Felipe A. MOLINA JAQUE, Ana RODRÍGUEZ-HERNÁNDEZ, Fuat ARIKAN, Diego LÓPEZ BERMEO, Alejandro TOMASELLO

Department of Neurological Surgery, Vall d’Hebron University Hospital, Universidad Autónoma de Barcelona, Barcelona, Spain

Multiple cerebral arteriovenous malformations (AVMs) are a rare occurrence usually associated with defined genetic disorders or a family history of cerebrovascular disease. The remaining cases cannot be associated to a genetic pathogenesis and are considered idiopathic. We report an extremely unusual case nor genetic neither idiopathic, but linked to an anatomical intracranial venous variation. The patient presented two independent frontal AVMs associated with rostral hypoplasia of the superior sagittal sinus. This anatomical variation may have induced frontal venous hypertension (VHT) triggering the development of the two AVMs. Throughout this intriguing case, we discuss the role of VHT in AVM development.

KEY WORDS: Intracranial arteriovenous malformations; Superior sagittal sinus; Hypertension