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Minerva Endocrinologica 1999 June;24(2):87-90

Copyright © 1999 EDIZIONI MINERVA MEDICA

lingua: Inglese

Congenital hypopituitarism in a 48-year old adult. Natural course, hormonal study and MRI evidence

Pentimone F., Riccioni S., Del Corso L.


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A case of Congenital Hypopituitarism (CH) in an untreated 48 yr-old-man is reported. The hormonal studies demonstrated a panhypopituitarism and MR imaging revealed absence of pituitary stalk, small anterior pituitary remnant on the sella floor and ectopic neurohypophysis at the tuber cinereum. The pattern of hormonal responsiveness suggests that CH encompasses findings typical of primary anterior pituitary disease and those of hypothalamic dysfunction.

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