CASE REPORTS  CARDIAC SECTION 

The Journal of Cardiovascular Surgery 2004 February;45(1):35-8

Copyright © 2004 EDIZIONI MINERVA MEDICA

lingua: Inglese

Left ventricular outflow obstruction after Fontan procedure involving a patient with complete atrioventricular septal defects complicated by a small left ventricle

Senzaki H. ¹, Kobayashi T. ¹, Morsy M. ¹, Asano H. ², Kyo S. ², Yokote Y. ²

¹ Department of Pediatric Cardiology Saitama Heart Institute Saitama Medical School Hospital, Saitama, Japan 2 Department of Cardiovascular Surgery Saitama Heart Institute Saitama Medical School Hospital, Saitama, Japan

We report a 1-year-old girl who developed ventricular outflow tract obstruction early after a Fontan operation, necessitating surgical relief using the Damus-Kaye-Stansel procedure. The patient had a complete atrioventricular septal defect complicated by a muscular ventricular septal defect (VSD) and a small left ventricle, a morphology that has not previously been reported in cases of systemic outflow tract obstruction after the Fontan procedure. Postoperative systemic outflow obstruction must be considered as a possible sequela following Fontan surgery in patients with an atrioventricular septal defect and a small left ventricle.