CASE REPORT   

Minerva Respiratory Medicine 2023 March;62(1):50-3

DOI: 10.23736/S2784-8477.22.01997-0

Copyright © 2022 EDIZIONI MINERVA MEDICA

language: English

Acute respiratory failure due to cutis laxa pulmonary emphysema treated with high-flow nasal cannula

Tommaso PERAZZO ^{1, 2}, Alessandro PERAZZO ¹, Gianluca FERRAIOLI ¹, Teresa DIAZ DE TERAN ³, Monica GONZALES ³, Paolo BANFI ⁴, Antonello NICOLINI ^{1, 4} ✉

¹ Respiratory Diseases Unit, General Hospital, Sestri Levante, Genoa, Italy; ² Respiratory Diseases and Allergy Clinic, Genoa, Italy; ³ Division of Pulmonology, Hospital Universitario Marqués de Valdecilla, Santander, Spain; ⁴ Rehabilitation Pulmonology, IRCCS Don Gnocchi Foundation, Milan, Italy

Cutis laxa is a rare connective tissue disorder characterized by progressive loosening of the skin, associated with abnormalities of other organs such as the lung. We present a case of this disease with pulmonary emphysema and acute respiratory failure successfully treated with high-flow nasal cannula.

KEY WORDS: Pulmonary emphysema; Cutis laxa; Respiratory insufficiency; Cannula