CASE REPORTS   

Minerva Pediatrica 2007 February;59(1):53-6

Copyright © 2007 EDIZIONI MINERVA MEDICA

language: English

Occipital mega encephalocele. Case report

Vergara G. ¹, Vergara P. ²

¹ Unit of Neonatology and Pediatrics A. Maresca Hospital, ASL Napoli 5, Naples, Italy 2 Department of Neurosurgery Federico II University, Naples, Italy

Encephalocele is a central nervous system malformation characterized by the herniation of the intracranial structures through a bony defect of the skull table. This is a case of a newborn female with a mega occipital encephalocele due to herniation of a part of the ventricular system. Urgent resection of the encephalocele and reconstruction of the meningeal and bone sheaths were performed. Nonetheless encephalocele has a poor prognosis and the surgical resection of particularly voluminous herniated masses can usually provoke severe deficits . The little patient, at discharge, one month after surgery, fed spontaneously and her motility was conserved