CLINICAL CASES   Free access

Minerva Anestesiologica 2003 July-August;69(7-8):641-5

Copyright © 2003 EDIZIONI MINERVA MEDICA

language: English, Italian

Anaestethic problems in Sanfilippo syndrome. A rare case of adult patient

Ingrosso M., Picilli M. M., Capasso A., Cecere F., Cirillo V., Merolla V.

¹ Operative Unit of Anesthesia and Resuscitation S.Maria della Speranza Hospital, Battaglia (SA), Italy 2 Department of Anesthesiological, Surgical and Emergency Sciences University Polyclinic Second University of Naples, Naples, Italy

The authors report the case of a female patient (41 years old) affected by mucopolysaccharidosis type III or Sanfilippo syndrome submitted to a gynecologic surgical procedure and describe the main anesthesiologic problems. A sub-arachnoid anesthesia with hyperbaric Bupivacain 0.5% was used. This technique proved to be safe and convenient without peri- and postoperative complications.