CLINICAL CASES   

Gazzetta Medica Italiana Archivio per le Scienze Mediche 2001 June;160(3):111-2

Copyright © 2001 EDIZIONI MINERVA MEDICA

language: English

Infantile nephrotic syndrome-diffuse mesangial sclerosis type A. Case report

Vanikar A. ¹, Patel R. ¹, Gera D. N. ²

¹ Department of Pathology, Laboratory Medicine and Transfusion Services; ² Department of Paediatric Nephrology, Institute of Kidney Diseases and Research Centre (IKDRC), Institute of Transplantation Sciences (ITS), Civil H Hospital Campus, Ahmedabad-380016, Gujarat, India

Infan­tile neph­rotic syn­drome (NS) ­with dif­fuse mesan­gial scler­osis (MS) is a ­rare dis­tinct cli­nic­o­path­o­logic ­entity pro­gressing to end-­stage ­renal ­failure ­before the ­patient is 3 ­years old. Trans­plan­ta­tion ­offers a ­viable alter­na­tive to all oth­er­wise ­fatal dis­order. We ­report a 15-­month-old ­female ­child ­with end-­stage ­renal ­failure sec­on­dary to infan­tile NS-dif­fuse mesan­gial scler­osis ­type to ­which she suc­cumbed ­before ­renal replace­ment ­therapy ­could be insti­tuted.