CASE REPORT   Open access

Italian Journal of Emergency Medicine 2022 April;11(1):37-40

DOI: 10.23736/S2532-1285.22.00113-6

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language: English

Moyamoya disease: a clinical case

Stefania MANTUANO ✉

Department of Emergency Medicine and Trauma Surgery, Grande Ospedale Metropolitano “Bianchi Melacrino Morelli”, Reggio Calabria, Italy

A 13-year-old male came to our Emergency Room for suspicion of stroke. When the young patient arrived, he presented left hemiplegia with a deflection of the buccal rhyme. He reported that, when he was at home, he suffered from a severe headache and, after that, he fell to the ground from a sudden loss of strength of the left hemisoma. He was rapidly subjected to a nuclear magnetic resonance to the brain and to the brain stem, which showed an area of restriction of the diffusivity in the right nuclear capsular area, compatible with an ischemic event. Admitted to the Neurology department, the patient underwent an angiographic study that documented a classic “cloud of smoke” appearance of the arteries placed at the base of the brain. The diagnosis of Moyamoya disease was therefore placed.

KEY WORDS: Moyamoya disease; Angiogenesis inducing agents; Stroke; Angiography; Intracranial hemorrhage