CASE REPORT   

Chirurgia 2020 October;33(5):260-2

DOI: 10.23736/S0394-9508.19.05004-6

Copyright © 2019 EDIZIONI MINERVA MEDICA

language: English

Surgical treatment of a patient with the diagnosis of arrhythmogenic right ventricular dysplasia

Farid GOJAYEV ¹, Huseyin A. SOLGUN ² ✉

¹ Department of Pediatric Cardiovasculer Surgery, Medical Park Bahcelievler Hospital, Istanbul, Turkey; ² Department of Pediatrics, Altınbas University Medical Park Bahcelievler Hospital, Istanbul, Turkey

Arrhythmogenic right ventricular dysplasia (ARVD) is a genetic heart disease that causes sudden deaths, especially in young people. Generally, right ventricle and left ventricular myocardial tissue are replaced with fat and fibrosis. Sudden death, rhythm disorders and heart failure in young ages are the most important symptoms of the disease. It is responsible for approximately 20% of sudden deaths in young people and the annual sudden death rate is 1-2%. Early diagnosis and treatment in people with a family history increases the quality of life. The diagnostic criteria for the diagnosis of the disease are divided into two groups as major and minor.2 major or 1 major + 2 minor criteria is sufficient for diagnosis. The diagnosis of the disease is made by the use of history, physical examination, electrocardiogram, echocardiography, 24-hour rhythm holter monitoring, right ventricular angiography, cardiac MRI, endomyocardial biopsy methods. According to the clinical course of the disease, antiarrhythmic drug, implanted cardioverter defibrillator (ICD), radiofrequency ablation and surgery are recommended. In this study, we present the both surgical treatment method and ICD implantation to a male patient with a family history of ARVD.

KEY WORDS: Arrhythmogenic right ventricular dysplasia; Tachycardia, ventricular, Surgery