CASE REPORTS   

Italian Journal of Maxillofacial Surgery 2010 August;21(2):107-10

Copyright © 2010 EDIZIONI MINERVA MEDICA

language: English

Extraskeletal myxoid chondrosarcoma of the maxilla: a case report

Caramanna B., Caramanna C., Briganti A., Braconi A., Solazzo L.

Division of Maxillofacial Surgery, ARNAS Civico, Di Cristina e Benfratelli, Palermo, Italy

The extraskeletal myxoid chondrosarcoma (EMC), described as a phenotypically and genotypically distinctive entity in 1972, is a sarcoma of soft tissue characterized by a protracted clinical course. Its incidence in the maxillo-facial location is very rare; in the literature only few cases are reported. The authors discuss a case of EMC, characterized by aspects of dedifferentiation, localized at the right half of the maxilla underlining the importance of the immunohistochemical investigations.