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SKIN INVOLVEMENT IN CONNECTIVE TISSUE DISEASES
Giornale Italiano di Dermatologia e Venereologia 2014 October;149(5):519-24
Copyright © 2014 EDIZIONI MINERVA MEDICA
language: English
An update on juvenile dermatomyositis
Boccaletti V., Di Nuzzo S., Feliciani C., Fabrizi G., Pagliarello C. ✉
Clinica Dermatologica, Università degli Studi di Parma, Parma, Italia
Juvenile dermatomyositis (JDM) is a rare, severe, autoimmune disease characterized by a small-vessel vasculopathy that primarily affects skin and muscle, but also lung, joints, gut and heart. Nowadays prompt recognition of this entity and aggressive treatment, when needed, improves outcomes and has decreased mortality that, before corticosteroid became a mainstay in therapy, could reach 40%.