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Indexed/Abstracted in: EMBASE, Scopus
Online ISSN 1827-188X
Porcu A., Taborelli G.
Istituto G. Gaslini -Genova Divisione di Otorinolaringoiatria
The association between clinical tinnitus and myoclonus of the soft palate is a rare childhood syndrome of unclear etiology. The authors report the case of a 10-year-old patient with a 3-year history of clinical tinnitus and myoclonus of the soft palate. Diagnostic work-up included: EEG, CT, cerebral MRI, blink reflex, echo Doppler TSA, neurological examination, audiometric and impedance testing, auditory evoked potential study, and ECG. Physical examination and blood chemistry tests were normal. The pathogenic mechanism was referable to associated clonic contracture of the malleus muscle (innervated by the trigeminal motor nerve branch) and the external stapedius muscle, which caused clicking from the opening and closing of the Eustachian tube and the rhythmic movement of the soft palate. In evaluating diagnostic and therapeutic approaches to the condition, treatment with drugs and/or invasive procedures is not recommended, because the symptoms tend to regress spontaneously and therapy has achieved poor results so far.