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GIORNALE ITALIANO DI DERMATOLOGIA E VENEREOLOGIA

A Journal on Dermatology and Sexually Transmitted Diseases


Official Journal of the Italian Society of Dermatology and Sexually Transmitted Diseases
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Giornale Italiano di Dermatologia e Venereologia 2001 February;136(1):63-6

language: Italian

“Morpheiform variant” dermatofibrosarcoma in a child. Description of a case

Vassilopoulou A., Betto P., Gennari E., Bonoldi E. *

Azienda Ospedaliera di Vicenza Divisione di Dermatologia
*Servizio di Anatomia Patologica


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Dermatofibrosarcoma protuberans (DFSP) is usually diagnosed during adult life at a tumoral stage, only rarely in childhood. Several unusual clinical and pathological variants of this neoplasm have been described, including the atrophic variant. We describe a 9 years old boy with a scarred, indurated lesion on the trunc of six years duration, which clinically resembled morphea. Histological examination showed typical features of dermatofibrosarcoma protuberans. The patient was treated with surgical excision of the tumor and wide margins of healthy tissue. Six years after removal of the lesion he is in good healt, free of recurrence. The recognition of the neoplasm is initially difficult because of the long clinical course of the lesion, that at the beginning appears like an apparently benign atrophic, morpheaform or cheloidal plaque. DFSP in childhood is probably under-estimated. Better knowledge of the initial appearance is important for an early diagnosis and easier surgical treatment.

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