Total amount: € 0,00
Official Journal of the Italian Society of Dermatology and Sexually Transmitted Diseases
Indexed/Abstracted in: EMBASE, PubMed/MEDLINE, Science Citation Index Expanded (SciSearch), Scopus
Impact Factor 1,014
Online ISSN 1827-1820
Menni S., Boccardi D.
Università degli Studi - Milano Istituto di Scienze Dermatologiche IRCCS - Ospedale Maggiore - Milano
A 16 year-old girl, with “disabling pansclerotic morphea”, presented recurrent intestinal bleeding. The patient, at the age of eleven, was suffering from severe musculo-skeletal atrophy of the left arm with severe sclerosis, and mild cutaneous sclerosis of the upper thorax and right forearm. Only mesenteric angiography showed telangiectasias of jejunum circulation. After a transfusion the patient was treated with progesterone/oestrogen combination with good result. “Disabling pansclerotic morphea” is usually associated with mild, non progressive visceral changes. Vascular ectasias is described only in systemic sclerosis and rarely in small bowel.