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Official Journal of the Italian Society of Dermatology and Sexually Transmitted Diseases
Indexed/Abstracted in: EMBASE, PubMed/MEDLINE, Science Citation Index Expanded (SciSearch), Scopus
Impact Factor 1,014
Online ISSN 1827-1820
Passarini B. 1, Lehmann J. 1, Varotti E. 1, Fanti P. A. 1, Pasquinelli G. 2
1 Università degli Studi - Bologna, Dipartimento di Medicina Clinica Specialistica e Sperimentale - Sezione di Clinica Dermatologica;
2 Servizio di Patologia e Diagnostica Ultrastrutturale Dipartimento di Patologia Sperimentale
Pigmented dermatofibrosarcoma protuberans is a rare neoplasm originating in the dermis. In rather 5% of the cases it contains dendritic melanocytes and is known as Bednar tumor.
The case of a 31 year-old man with a plaque-like lesion in the sacral region is described. On histological examination, a dermal neoplasm compound of spindle cells and pigmented cells penetrating the subcutaneous tissue but not reaching the epidermidis is observed. The diagnosis of Bednar tumor is made.
The histogenesis of DFSP is discussed and the conclusion is drawn for the dualistic histogenetical hypothesis of the neoplasm on the basis of electron microscopy and immunohistochemical studies.