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A Journal on Surgery
Indexed/Abstracted in: EMBASE, Scopus, Emerging Sources Citation Index
Chirurgia 2005 October;18(5):405-8
Giant desmoid tumors in Gardner's syndrome. A case report and review of the literature
Cobianchi L., Zonta S., Lovisetto F., Jemos V., Alessiani M., Sgarella A., Dionigi P.
Desmoid tumors are very rare and occur non-sporadically as a phenotypic variant of familial adenomatous polyposis (FAP). In this syndrome, desmoid tumors are particularly aggressive and are the second cause of death. The literature reveals that the difficulty in choosing the therapeutic strategy for these tumors is due to their location and frequent habit of recurring. We report the case of a patient with Gardner's syndrome who had already undergone a prophylactic total colectomy and then presented huge desmoid masses in his abdomen. He has been treated successfully with surgery in our Center. This experience provides support to the prevailing but still debated belief that surgery is a suitable management for these tumors.